Over Restriction of Dietary Protein Allowance: The Importance of Ongoing Reassessment of Natural Protein Tolerance in Phenylketonuria

Phenylalanine (Phe) tolerance is highly variable in phenylketonuria (PKU) and rarely described in patients aged ≥12 years. Patients ≥12 years of age with PKU were systematically challenged with additional natural protein (NP) if blood Phe levels remained below 480 µmol/L (i.e., upper target blood Ph...

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Bibliographic Details
Main Author: Pinto, Alex (author)
Other Authors: Almeida, Manuela Ferreira (author), MacDonald, Anita (author), Ramos, Paula Cristina (author), Rocha, Sara (author), Guimas, Arlindo (author), Ribeiro, Rosa (author), Martins, Esmeralda (author), Bandeira, Anabela (author), Jackson, Richard (author), van Spronsen, Francjan (author), Payne, Anne (author), Rocha, Júlio César (author)
Format: article
Language:eng
Published: 2020
Subjects:
BH4
natural protein tolerance
phenylketonuria
phenylalanine
Online Access:http://hdl.handle.net/10400.16/2427
Country:Portugal
Oai:oai:repositorio.chporto.pt:10400.16/2427

Internet

http://hdl.handle.net/10400.16/2427

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