Over Restriction of Dietary Protein Allowance: The Importance of Ongoing Reassessment of Natural Protein Tolerance in Phenylketonuria

Phenylalanine (Phe) tolerance is highly variable in phenylketonuria (PKU) and rarely described in patients aged ≥12 years. Patients ≥12 years of age with PKU were systematically challenged with additional natural protein (NP) if blood Phe levels remained below 480 µmol/L (i.e., upper target blood Ph...

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Detalhes bibliográficos
Autor principal: Pinto, Alex (author)
Outros Autores: Almeida, Manuela Ferreira (author), MacDonald, Anita (author), Ramos, Paula Cristina (author), Rocha, Sara (author), Guimas, Arlindo (author), Ribeiro, Rosa (author), Martins, Esmeralda (author), Bandeira, Anabela (author), Jackson, Richard (author), van Spronsen, Francjan (author), Payne, Anne (author), Rocha, Júlio César (author)
Formato: article
Idioma:eng
Publicado em: 2020
Assuntos:
BH4
natural protein tolerance
phenylketonuria
phenylalanine
Texto completo:http://hdl.handle.net/10400.16/2427
País:Portugal
Oai:oai:repositorio.chporto.pt:10400.16/2427

Texto Completo

http://hdl.handle.net/10400.16/2427

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