Bioenergetic dysfunction in Huntington's disease human cybrids

In this work we studied the mitochondrial-associated metabolic pathways in Huntington's disease (HD) versus control (CTR) cybrids, a cell model in which the contribution of mitochondrial defects from patients is isolated. HD cybrids exhibited an interesting increase in ATP levels, when compared...

Full description

Bibliographic Details
Main Author: Ferreira, I. Luísa (author)
Other Authors: Cunha-Oliveira, Teresa (author), Nascimento, Maria V. (author), Ribeiro, Márcio (author), Proença, M. Teresa (author), Januário, Cristina (author), Oliveira, Catarina R. (author), Rego, A. Cristina (author)
Format: article
Language:por
Published: 2011
Online Access:http://hdl.handle.net/10316/84852
Country:Portugal
Oai:oai:estudogeral.sib.uc.pt:10316/84852